PUOTI, Gianfranco
 Distribuzione geografica
Continente #
EU - Europa 2.929
NA - Nord America 2.049
AS - Asia 1.796
SA - Sud America 471
AF - Africa 22
OC - Oceania 6
Continente sconosciuto - Info sul continente non disponibili 4
Totale 7.277
Nazione #
US - Stati Uniti d'America 2.017
RU - Federazione Russa 1.048
SG - Singapore 670
IE - Irlanda 644
CN - Cina 467
BR - Brasile 419
HK - Hong Kong 336
IT - Italia 294
UA - Ucraina 280
GB - Regno Unito 229
DE - Germania 164
VN - Vietnam 103
FI - Finlandia 82
GR - Grecia 58
KR - Corea 47
SE - Svezia 45
TR - Turchia 43
IN - India 34
FR - Francia 26
AR - Argentina 25
BD - Bangladesh 17
JP - Giappone 17
CA - Canada 16
AT - Austria 15
BE - Belgio 15
EC - Ecuador 12
IQ - Iraq 12
PK - Pakistan 11
MX - Messico 8
NL - Olanda 8
UZ - Uzbekistan 7
ID - Indonesia 6
MY - Malesia 6
ZA - Sudafrica 6
JO - Giordania 5
AZ - Azerbaigian 4
EU - Europa 4
KE - Kenya 4
PL - Polonia 4
VE - Venezuela 4
AL - Albania 3
AU - Australia 3
BG - Bulgaria 3
CO - Colombia 3
CR - Costa Rica 3
CZ - Repubblica Ceca 3
MA - Marocco 3
NZ - Nuova Zelanda 3
PY - Paraguay 3
BY - Bielorussia 2
CL - Cile 2
ES - Italia 2
IR - Iran 2
NI - Nicaragua 2
PH - Filippine 2
PT - Portogallo 2
SN - Senegal 2
TN - Tunisia 2
AE - Emirati Arabi Uniti 1
BB - Barbados 1
BO - Bolivia 1
CI - Costa d'Avorio 1
DK - Danimarca 1
DO - Repubblica Dominicana 1
DZ - Algeria 1
EG - Egitto 1
ET - Etiopia 1
HU - Ungheria 1
IL - Israele 1
JM - Giamaica 1
KW - Kuwait 1
LA - Repubblica Popolare Democratica del Laos 1
LY - Libia 1
NP - Nepal 1
OM - Oman 1
PE - Perù 1
TW - Taiwan 1
UY - Uruguay 1
Totale 7.277
Città #
Dublin 641
Jacksonville 419
Hong Kong 336
Moscow 334
Santa Clara 333
Singapore 212
Chandler 196
Princeton 96
Beijing 76
Roxbury 75
Ann Arbor 68
Medford 64
New York 56
Seoul 45
Ashburn 42
Wilmington 40
Hefei 37
Ho Chi Minh City 36
Boardman 35
Cambridge 34
Nanjing 34
Jinan 32
São Paulo 31
Caserta 30
Woodbridge 30
Munich 28
Bremen 26
San Mateo 25
The Dalles 25
Des Moines 21
Hanoi 21
Milan 19
Bengaluru 16
Shenyang 16
Brussels 15
Dallas 15
Rio de Janeiro 14
Zhengzhou 14
Los Angeles 13
Redwood City 13
Hangzhou 12
Nuremberg 12
Siano 12
Hebei 11
Brasília 10
Helsinki 10
Curitiba 9
San Francisco 9
Tianjin 9
Belo Horizonte 8
Guangzhou 8
Naples 8
Napoli 8
Ningbo 8
Taiyuan 8
Haiphong 7
Lanzhou 7
Quito 7
Rome 7
Tashkent 7
Vienna 7
Boydton 6
Falkenstein 6
Guidonia 6
Houston 6
Mountain View 6
Porto Alegre 6
Ranchi 6
Auburn Hills 5
Baghdad 5
Caxias do Sul 5
Changsha 5
Dhaka 5
Duque de Caxias 5
Ipoh 5
London 5
Norwalk 5
Taizhou 5
Turku 5
Amman 4
Baku 4
Campinas 4
Capua 4
Carapicuíba 4
Erbil 4
Fairfield 4
Feira de Santana 4
Guarulhos 4
Haikou 4
Jiaxing 4
Limbiate 4
Praia Grande 4
Rio Grande 4
Andover 3
Betim 3
Cleveland 3
Da Nang 3
Düsseldorf 3
Falconara Marittima 3
Guayaquil 3
Totale 3.971
Nome #
A cluster of progranulin C157KfsX97 mutations in Southern Italy: clinical characterization and genetic correlations 131
Atypical Progressive Multifocal Leukoencephalopathy in a Kidney Transplant Recipient With Improving Symptoms After Immunocompetence Recovery 126
Creutzfeldt-Jakob disease (CJD) in italian patients with PRNP V210I mutation: an epidemiological and clinical evaluation 119
A comparison of Tau and 14-3-3 protein in the diagnosis of Creitzfeldt-Jakob disease 111
12-months prospective Pentraxin-3 and metabolomic evaluation in multiple sclerosis patients treated with glatiramer acetate 109
Delayed post‐hypoxic leukoencephalopathy with a peculiar autoantibody association 108
Creutzfeldt-Jakob disease with a novel extra-repeat insertional mutation in the PRNP gene 107
A Novel Missense Mutation in CAV3 Gene in an Italian Family With Persistent hyperCKemia, Myalgia and Hypercholesterolemia: Double-trouble 107
Amyloid-beta42 interacts mainly with insoluble prion protein in the Alzheimer brain 101
Is the pathology of posterior cortical atrophy clinically predictable? 99
A novel insertional mutation in the prion protein gene: clinical and bio-molecular findings. 95
Co-existence of PrP D Types 1 and 2 in Sporadic Creutzfeldt-Jakob Disease of the VV Subgroup: Phenotypic and Prion Protein Characteristics 95
Human prion diseases: Surgical lessons learned from iatrogenic prion transmission 94
A novel SLC20A2 gene mutation causing primary familial brain calcification in an Ukrainian patient. 94
Rehabilitation of gesture imitation: a case study with fMRI. 92
A cluster of progranulin C157KfsX97 mutation in southern Italy- clinical characterization and genetic correlations 92
Studio clinico, neuropatologico e bio-molecolare della malattia di Creutzfeldt-Jakob associata a mutazione V210I del gene della proteina prionica 91
Myopathic changes in neurofibromatosis type 1 91
A case of Kohlmeier-Degos disease with dramatic neurological involvment 90
Sporadic human prion diseases: molecular insights and diagnosis 89
Deterioramento Cognitivo Minimo: analisi dei fattori di rischio e del tasso di progressione verso la demenza 89
Creutzfeldt-Jakob disease: topography of PrPres immunoreactivity 89
LA NEUROMIELITE OTTICA È UN’ ASSOCIAZIONE SINDROMICA COMUNE A PATOLOGIE ETEROGENEE 87
Protease-sensitive prions with 144-bp insertion mutations 86
Alemtuzumab-Related Lymphocyte Subset Dynamics and Disease Activity or Autoimmune Adverse Events: Real-World Evidence 85
A mutation in the 5'-UTR of GRN gene associated with frontotemporal lobar degeneration: phenotypic variability and possible pathogenetic mechanisms 84
Heidenhain variant of Creutzfeldt-Jakob disease with the co-occurrence of two differents types of prion proteins 83
Clinical and Genetic Heterogeneity in a Large Family with Pseudoxanthoma Elasticum: MTHFR and SERPINE1 Variants as Possible Disease Modifiers in Developing Ischemic Stroke 83
Coexistence of cavernous hemangioma and other vascular malformations of the orbit. A report of three cases 81
phenotypic heterogeneity in Creutzfeldt-Jakob disease associated with a new prion protein mutation 81
Analyses of the Protein Tau to Help Determine Whether the Newly Discovered Protease-Sensitive Prionopathy is the Sporadic Form of Gerstmann-Sträussler-Scheinker Disease (GSS) 81
CORRELATI CLINICO-STRUMENTALI IN UN CASO DI CREUTZFELD- JACOB A LUNGA SOPRAVVIVENZA. 81
Migraine as possible red flag of PFO presence in suspected demyelinating disease 81
Systematic Review on the Role of Lobar Cerebral Microbleeds in Cognition 80
Dalla malattia di Schilder all’adrenoleucodistrofia; una breve storia di un secolo di ricerca neuropatologica clinica esemplare 79
The Rise of the GRN C157KfsX97 Mutation in Southern Italy: Going Back to the Fall of the Western Roman Empire 79
Insertional mutation in prion protein gene presenting with schizophrenia 77
Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein. 75
Fas-L expression in sporadic Creutzfeldt-Jakob disease: an immunohistochemistry study 75
Non-alcoholic acute Wernicke's encephalopathy: Role of MRI in non typical cases. 75
Fas-L is expressed in sporadic Creutzfeldt-Jakob Disease 74
Minimally invasive percutaneous treatment for osteoid osteoma of the Spine. A case report 74
Slowly progressive JC positive multifocal leukoencephalopathy not associated with overt immunodeficency, oncohaematological disorder nor immunosoppressive therapies 73
A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease 73
Hereditary cerebral hemorrhage with amyloidosis associated with E693K mutation of APP 72
Variably Protease-sensitive Prionopathy in an Apparent Cognitively Normal 93-Year-Old 72
Creutzfeldt-Jakob Disease 72
Expanding the spectrum of SPTLC1-related disorders beyond hereditary sensory and autonomic neuropathies: a novel case of the distinct "S331 syndrome" 72
Case Report: Histopathology and Prion Protein Molecular Properties in Inherited Prion Disease With a De Novo Seven-Octapeptide Repeat Insertion 72
Creutzfeldt-Jakob disease: Carnoy's fixative improves the immunohistochemistry of the proteinase K-resistant prion protein 71
Experimental Therapy with Quinacrine in Creutzfeldt-Jakob disease 71
Progressive multifocal leukoencephalopathy presenting with bilateral myoclonus: a case report 71
Sporadic Creutzfeldt-Jakob disease: the extent of microglia activation is dependent on the biochemical type of PrPSc. 70
Microglia and complement in the cortex of Creutzfeldt-Jakob disease and comparison with Alzheimer’s disease 70
Creutzfeldt-Jakob disease with a novel four extra-repeat insertional mutation in the PrP gene 69
Experimental therapy with quinacrine in Creutzfeldt-Jakob diseases 69
Characterization of prion disease associated with a two-octapeptide repeat insertion 69
Heidenhain Variant of Sporadic Creutzfeldt-Jakob Disease With the Co-Occurrence of Two Different Types of Prion Protein 68
A peculiar report of rare multifocal "ganglio-glioneurocytoma" 68
MRI "fogging" in cerebellar ischaemia: case report 67
Variably Protease-Sensitive Prionopathy: a Novel Disease of the Prion Protein 67
Tau protein in a novel prion disease with GSS features 67
Creutzfeldt-Jakob disease (CJD) associated with V210I PRNP mutation: phenotypic and molecular genetic analysis 67
Heidenhain variant in two patients with inherited V210I Creutzfeldt-Jakob disease 67
Sporadic Creutzfeldt-Jakob disease: co-occurrence of different types of PrP(Sc) in the same brain 66
Creutzfeldt-Jakob disease: Distinct PrPres types induce different microglial reaction patterns 66
Synthetic Aβ peptides acquire prion-like properties in the brain 66
Large anterior temporal Virchow–Robin spaces: Evaluating MRI features over the years—Our experience and literature review 66
The epsilon isoform of 14-3-3 protein is a component of the prion protein amyloid deposits of Gerstmann-Sträussler-Scheinker disease. 65
Tauopathies: a new phenotype with epilepsy and severe cerebellar involvement 65
Identical large scale rearrangement of mitochondrial DNA causes Kearns-Sayre syndrome in a mother and her son 63
NOVEL HUMAN PRION DISEASE AFFECTING 3 PRION CODON 129 GENOTYPES: THE SPORADIC FORM OF GERSTMANN-STRÄUSSLER-SCHEINKER DISEASE? 63
“Borderline” idiopathic CD4+ T-cell lymphocytopenia presenting with atypical progressive multifocal leukoencephalopathy 62
Sporadic Creutzfeldt - Jakob disease’ 61
Global-local information processing in an unusual patient with posterior cortical atrophy 61
Sporadic cCreutzfeldt-Jakob disease: coexistence of type 1 and type 2 PrPSc in the same brain 60
SPORADIC CEREUTZFELDT-JAKOB DISEASE WITH MM1-TYPE PRION PROTEIN AND PLAQUES 59
Creutzfeldt-Jakob disease with one extra-repeat insertion in PRNP 59
Polymorphism at codon 129 of PRNP affects the phenotypic expression of Creutzfeldt-Jakob disease linked to E200K mutation 58
Disordini di movimento nella patologia neurologica dell’anziano 58
Early Onset Atypical Dementia Associated with a Novel Seven Octapeptide Repeat Insertion in the Prion Protein Gene 58
Molecular Bases of Phenotypic Heterogeneity in Prion Diseases 58
New-onset refractory status epilepticus mimicking herpes virus encephalitis 57
Plasma Small Extracellular Vesicle Cathepsin D Dysregulation in GRN/C9orf72 and Sporadic Frontotemporal Lobar Degeneration 56
Phenotypic Heterogeneity and Type-1/2 PrPSc Co-Occurrence in Creutzfeldt-Jakob Disease Associated With a new Mutation of PRNP 56
Sporadic Creutzfeldt-Jakob disease: coexistence of biochemically distinct types of PrPSc in the same brain 56
Protease-Sensitive Prionopathy in a Cognitively Normal 93 Year Old 56
Sporadic Creutzfeldt-Jakob disease in a native Puerto Rican patient 56
tion in the prion protein genme presenting with schizophrenia 55
Topografic distribution of PrPres in Creutzfeldt-Jakob disease as revealed by immunohistochemistry 55
Singular cases of Alzheimer's disease disclose new and old genetic "acquaintances" 55
TOPOGRAPHIC DISTRIBUTION OF PRP-Res IN CREUTZFELDT-JAKOB DISEASE AS REVEALED BY IMMUNOHISTOCHEMISTRY 54
Dramatic neurological debut in a case of Köhlmeier-Degos disease 54
Predictive factors of volumetric reduction in lumbar disc herniation treated by O2-O3 chemiodiscolysis 54
Distinct types of PrPres induce different microglial reaction in sporadic Creutzfeldt-Jakob disease 53
Insertional mutation in prion protein gene presenting with schizophrenic-like symptoms 53
Unusual CLIPPERS presentation and role of MRI examination in the proper diagnostic assessment: A case report. 53
Plasma Small Extracellular Vesicles with Complement Alterations in GRN/C9orf72 and Sporadic Frontotemporal Lobar Degeneration 51
Pathological 25 kDa C-Terminal Fragments of TDP-43 Are Present in Lymphoblastoid Cell Lines and Extracellular Vesicles from Patients Affected by Frontotemporal Lobar Degeneration and Neuronal Ceroidolipofuscinosis Carrying a GRN Mutation 49
Totale 7.394
Categoria #
all - tutte 30.268
article - articoli 0
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 0
selected - selezionate 0
volume - volumi 0
Totale 30.268


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/2021349 0 0 0 0 0 7 84 69 2 86 77 24
2021/2022557 44 10 3 13 186 2 10 30 21 16 36 186
2022/20231.033 123 5 21 55 92 60 1 42 572 13 23 26
2023/2024432 32 11 18 26 159 61 7 2 2 7 28 79
2024/20251.510 5 20 11 54 244 157 150 119 251 305 112 82
2025/20262.150 140 177 219 305 474 835 0 0 0 0 0 0
Totale 7.394